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What is Cystic Fibrosis?

Cystic fibrosis (also known as pulmonary cystic fibrosis) is an inherited disease that causes serious damage to the lungs and digestive system by impairing the function of cells that produce mucus, sweat and digestive enzymes. In people with cystic fibrosis, the defective gene causes mucus in the bronchi to become thick and sticky. Although patients require daily care, they are in good condition to lead a normal life, the quality of which has greatly improved compared to previous years. The introduction of screening, modern therapies and rehabilitation treatments has made most people with cystic fibrosis reach the age of 40-50.

In cystic fibrosis, symptoms may vary depending on the severity of the disease. In some people, the disease gradually progresses causing deterioration of lung and digestive function. In others, however, symptoms can only occur in adolescence or adulthood. Patients with cystic fibrosis have higher than normal levels of sodium chloride in their sweat and are more at risk for unusual symptoms such as pancreatitis, diabetes or infertility.

That special body care at pregnant bleeding

Women often neglect themselves during pregnancy because they feel physically unattractive. They forget that special body care at this particular time not only improves the mood pregnant bleeding, but also influences the condition of our figure after childbirth.

A proper diet and large amounts of still mineral water, juices, as well as giving up tea (possibly herbal) and coffee are very important with pregnant bleeding. The diet should be rich in all nutrients, including fats.

In the second trimester of pregnancy, the hormonal storm calms down a bit, most pregnant women feel best now pregnant bleeding and now you can go to the beauty salon. It is always best to consult your pregnancy doctor and inform them pregnant bleeding of your intention to visit a beauty salon.

Pregnancy is a special state, so I recommend pregnant women:

  • walks
  • exercises in fitness clubs for expectant mothers (they prepare muscles for childbirth)
  • a variety of diet
  • lots of rest
  • little stress
  • getting into the habit of regular home body and face care
  • visits to a beautician
  • a lot of peace and “taking it easy”.

Besides, we, as parents with pediatrics day and night

Besides, we, as parents with pediatrics day and night

It’s also important to stick to one doctor. Because then he knows EXACTLY the medical history of our child and the child in general. Besides, we, as parents, also have the comfort that the doctor knows our approach to parenting, views related to it, etc. Our pediatrician knows pediatrics day and night, for example, that when I call him, the matter must be serious, and when my husband calls , ie that in my opinion it was not necessary to call.

HE IS AN EXPERIENCED DOCTOR
Check where he worked before, where he gained experience pediatrics day and night and education. Our pediatrician is the founder of the Wrocław Hospice for Children. This gave me a wide-spectrum image of him, not only as a doctor but also as a human being.

HAS A GOOD FEEDBACK AMONG OTHER PARENTS.
In the age of the Internet, it is not difficult. Maybe we do not really mean the Znany Lek portal and local opinions pediatrics day and night (sometimes written not necessarily by patients), but about conversations with parents, e.g. on local parenting groups. It is a treasure trove of knowledge.

YOU CAN ASK HIM ANY QUESTION.
Coming from the doctor’s office, you must not feel ignorant.
When going to him, write down all the questions, ask them and expect answers. If it rains but you don’t understand it, ask. The parent needs to know what the child is suffering from, what is happening to him, what he can expect, what symptoms are worrying, why exactly such treatment or why not.

A good pediatrician is essential. He is a doctor not only for your child pediatrics day and night, but also for you. It has to be a person who can really understand and calm you down. He will not scoff when you come with a bubble on a child’s hand, fearing that it is certainly some kind of contagious disease, while it will only be a mosquito bite. A good pediatrician is also a good psychologist and a helping hand. It is a support for your and your baby’s nerves.

Does it have to do with sclerodactyly?

Phase I clinical trial was conducted by a group of scientists from France. The method used is based on obtaining stem sclerodactyly and regenerative cells from adipose tissue, and then applying them to the disease sites, into the fibrotic tissue and into the ischemic areas, to initiate the repair process.

In patients with systemic sclerosis, the typical clinical symptom is sclerodactyly, often accompanied by contractures in the small joints of the hands. In addition, chronic ischemia with severe pain is present in the hands, skin ulcerations and superficial subcutaneous calcium deposits are often present. Therapies sclerodactyly used so far in systemic sclerosis are focused on improving the organ related complications of the disease. Meanwhile, changes in the hands have a significant impact on the limitation in the functioning of the patient and in the performance of daily activities, moreover, they cause severe pain and significantly affect the quality of life.

The study was open-ended, the procedure was performed in 12 women with systemic sclerosis and significant hand dysfunction assessed on the basis of the Cochin Hand Function Score. The procedure was performed under general anesthesia sclerodactyly. After liposuction, the obtained material was automatically processed in order to obtain the stromal vascular fraction (SFV). Subsequently, subcutaneous injections were made along the lateral surfaces of each finger, introducing approximately 0.5 ml of SFV into the vicinity of the neurovascular bundle.

Respiratory symptoms

Dense and sticky mucus associated with cystic fibrosis is found in the bronchioles, which supply air to the lungs. This causes:

  • Chronic wet cough, especially in the morning.
  • Wheezing
  • Dyspnoea
  • Poor tolerance of exercise
  • Recurrent pneumonia
  • Sinusitis, nasal polyps.

Respiratory symptoms

Gastrointestinal symptoms

The symptoms stem from blocked ducts that digestive enzymes send from the pancreas to the small intestine. Lack or deficiency of enzymes means that the intestines cannot fully absorb nutrients from the food they consume. The result is often:

  • Stinking, oily stools
  • Poor weight and height gain
  • Abdominal pain, flatulence
  • Bowel obstruction, especially in newborns
  • Severe constipation, which in extreme cases can cause rectal prolapse
  • Cystic fibrosis carries many complications from both respiratory, gastrointestinal and reproductive systems.

Respiratory complications:

  • Airway damage (so-called bronchiectasis)
    It is one of the most common complications of cystic fibrosis.
  • Chronic infections
    The dense mucus in the lungs and sinuses is an excellent medium for bacteria and fungi. Cystic fibrosis patients are more likely to develop pneumonia, bronchitis or sinus infections.
  • Nasal polyps
    Chronic inflammation and swelling of mucous membranes in the nose contribute to the development of polyps that can make breathing difficult during sleep.
  • Blood spitting (so-called haemoptysis))
    Cystic fibrosis can cause a decrease in the thickness of the airway walls. As a result, sufferers can spit out secretions from the blood.
  • Pneumothorax
    The condition, in which air leaks into the pleura, is also more common in older people with cystic fibrosis. It can cause chest pain and shortness of breath.
  • Respiratory failure
    As the disease progresses, damage to the lung tissue progresses leading to gradual hypoxia of the tissues and the whole body, which can be life-threatening as a result.

 


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